Amino acid and derivative metabolism
Häussinger D. Liver glutamine metabolism. JPEN J Parenter Enteral Nutr. 1990 Jul;14(4 Suppl):56S–62S. doi: 10.1177/014860719001400405. PMID: 2205732.; Owen OE, Reichard GA, Patel MS, Boden G. Energy metabolism in feasting and fasting. Adv Exp Med Biol. 1979;111():169–88. doi: 10.1007/978-1-4757-0734-2_8. PMID: 371355.; Felig P. Amino acid metabolism in man. Annu Rev Biochem. 1975;44():933–55. doi: 10.1146/annurev.bi.44.070175.004441. PMID: 1094924.
Metabolites
N(6),N(6),N(6)-trimethyl-L-lysine zwitterion
Formula: C9H21N2O2 (189.16029460000001)
CAS ID: 19253-88-4
Enzyme
| EC Number | name | full name | note |
|---|---|---|---|
| 1.-.-.- | |||
| 1.1.1.159 | 7alpha-hydroxysteroid dehydrogenase | 7alpha-hydroxysteroid:NAD+ 7-oxidoreductase | |
| 1.1.1.178 | 3-hydroxy-2-methylbutyryl-CoA dehydrogenase | (2S,3S)-3-hydroxy-2-methylbutanoyl-CoA:NAD+ oxidoreductase | |
| 1.1.1.239 | 3alpha(17beta)-hydroxysteroid dehydrogenase (NAD+) | 3alpha(or 17beta)-hydroxysteroid:NAD+ oxidoreductase | |
| 1.1.1.31 | 3-hydroxyisobutyrate dehydrogenase | 3-hydroxy-2-methylpropanoate:NAD+ oxidoreductase | |
| 1.1.1.35 | 3-hydroxyacyl-CoA dehydrogenase | (S)-3-hydroxyacyl-CoA:NAD+ oxidoreductase | |
| 1.1.1.37 | malate dehydrogenase | (S)-malate:NAD+ oxidoreductase | |
| 1.1.1.399 | 2-oxoglutarate reductase | (R)-2-hydroxyglutarate,NAD+ 2-oxidireductase | |
| 1.1.1.53 | 3alpha(or 20beta)-hydroxysteroid dehydrogenase | 3alpha(or 20beta)-hydroxysteroid:NAD+ oxidoreductase | |
| 1.1.1.62 | 17beta-estradiol 17-dehydrogenase | 17beta-estradiol:NAD(P)+ 17-oxidoreductase | |
| 1.1.1.79 | glyoxylate reductase (NADP+) | glycolate:NADP+ oxidoreductase | |
| 1.1.1.81 | hydroxypyruvate reductase | D-glycerate:NADP+ 2-oxidoreductase | |
| 1.1.1.95 | phosphoglycerate dehydrogenase | 3-phospho-D-glycerate:NAD+ 2-oxidoreductase | |
| 1.1.3.15 | (S)-2-hydroxy-acid oxidase | (S)-2-hydroxy-acid:oxygen 2-oxidoreductase | |
| 1.1.99.1 | choline dehydrogenase | choline:acceptor 1-oxidoreductase | |
| 1.11.1.2 | NADPH peroxidase | NADPH:hydrogen-peroxide oxidoreductase | |
| 1.11.1.8 | iodide peroxidase | iodide:hydrogen-peroxide oxidoreductase | |
| 1.13.11.11 | tryptophan 2,3-dioxygenase | L-tryptophan:oxygen 2,3-oxidoreductase (decyclizing) | |
| 1.13.11.18 | persulfide dioxygenase | S-sulfanylglutathione:oxygen oxidoreductase | |
| 1.13.11.19 | cysteamine dioxygenase | 2-aminoethanethiol:oxygen oxidoreductase | |
| 1.13.11.20 | cysteine dioxygenase | L-cysteine:oxygen oxidoreductase | |
| 1.13.11.27 | 4-hydroxyphenylpyruvate dioxygenase | 4-hydroxyphenylpyruvate:oxygen oxidoreductase (hydroxylating, decarboxylating) | |
| 1.13.11.5 | homogentisate 1,2-dioxygenase | homogentisate:oxygen 1,2-oxidoreductase (decyclizing) | |
| 1.13.11.52 | indoleamine 2,3-dioxygenase | D-tryptophan:oxygen 2,3-oxidoreductase (decyclizing) | |
| 1.13.11.53 | acireductone dioxygenase (Ni2+-requiring) | 1,2-dihydroxy-5-(methylthio)pent-1-en-3-one:oxygen oxidoreductase (formate- and CO-forming) | |
| 1.13.11.54 | acireductone dioxygenase [iron(II)-requiring] | 1,2-dihydroxy-5-(methylthio)pent-1-en-3-one:oxygen oxidoreductase (formate-forming) | |
| 1.13.11.6 | 3-hydroxyanthranilate 3,4-dioxygenase | 3-hydroxyanthranilate:oxygen 3,4-oxidoreductase (decyclizing) | |
| 1.14.11.1 | gamma-butyrobetaine dioxygenase | 4-trimethylammoniobutanoate,2-oxoglutarate:oxygen oxidoreductase (3-hydroxylating) | |
| 1.14.11.8 | trimethyllysine dioxygenase | N6,N6,N6-trimethyl-L-lysine,2-oxoglutarate:oxygen oxidoreductase (3-hydroxylating) | |
| 1.14.13.148 | trimethylamine monooxygenase | N,N,N-trimethylamine,NADPH:oxygen oxidoreductase (N-oxide-forming) | |
| 1.14.13.8 | flavin-containing monooxygenase | N,N-dimethylaniline,NADPH:oxygen oxidoreductase (N-oxide-forming) | |
| 1.14.13.9 | kynurenine 3-monooxygenase | L-kynurenine,NADPH:oxygen oxidoreductase (3-hydroxylating) | |
| 1.14.16.1 | phenylalanine 4-monooxygenase | L-phenylalanine,tetrahydrobiopterin:oxygen oxidoreductase (4-hydroxylating) | |
| 1.14.16.2 | tyrosine 3-monooxygenase | L-tyrosine,tetrahydrobiopterin:oxygen oxidoreductase (3-hydroxylating) | |
| 1.14.17.1 | dopamine beta-monooxygenase | dopamine,ascorbate:oxygen oxidoreductase (beta-hydroxylating) | |
| 1.14.18.1 | tyrosinase | L-tyrosine,L-dopa:oxygen oxidoreductase | |
| 1.16.1.8 | [methionine synthase] reductase | [methionine synthase]-methylcob(III)alamin,S-adenosyl-L-homocysteine:NADP+ oxidoreductase | |
| 1.2.1.19 | aminobutyraldehyde dehydrogenase | 4-aminobutanal:NAD+ 1-oxidoreductase | |
| 1.2.1.27 | methylmalonate-semialdehyde dehydrogenase (CoA-acylating) | 2-methyl-3-oxopropanoate:NAD+ 3-oxidoreductase (CoA-propanoylating) | |
| 1.2.1.3 | aldehyde dehydrogenase (NAD+) | aldehyde:NAD+ oxidoreductase | |
| 1.2.1.31 | L-aminoadipate-semialdehyde dehydrogenase | L-2-aminoadipate-6-semialdehyde:NAD(P)+ 6-oxidoreductase | |
| 1.2.1.46 | formaldehyde dehydrogenase | formaldehyde:NAD+ oxidoreductase | |
| 1.2.1.47 | 4-trimethylammoniobutyraldehyde dehydrogenase | 4-trimethylammoniobutanal:NAD+ 1-oxidoreductase | |
| 1.2.1.8 | betaine-aldehyde dehydrogenase | betaine-aldehyde:NAD+ oxidoreductase | |
| 1.2.1.88 | L-glutamate gamma-semialdehyde dehydrogenase | L-glutamate gamma-semialdehyde:NAD+ oxidoreductase | |
| 1.2.3.5 | glyoxylate oxidase | glyoxylate:oxygen oxidoreductase | |
| 1.2.4.4 | 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring) | 3-methyl-2-oxobutanoate:[dihydrolipoyllysine-residue (2-methylpropanoyl)transferase]-lipoyllysine 2-oxidoreductase (decarboxylating, acceptor-2-methylpropanoylating) | |
| 1.21.1.1 | iodotyrosine deiodinase | NADP+:L-tyrosine oxidoreductase (iodinating) | |
| 1.21.99.3 | thyroxine 5-deiodinase | 3,3',5'-triiodo-L-thyronine,iodide:acceptor oxidoreductase (iodinating) | |
| 1.21.99.4 | thyroxine 5'-deiodinase | 3,3',5-triiodo-L-thyronine,iodide:acceptor oxidoreductase (iodinating) | |
| 1.3.8.1 | short-chain acyl-CoA dehydrogenase | short-chain acyl-CoA:electron-transfer flavoprotein 2,3-oxidoreductase | |
| 1.3.8.4 | isovaleryl-CoA dehydrogenase | 3-methylbutanoyl-CoA:electron-transfer flavoprotein oxidoreductase | |
| 1.3.8.5 | short-chain 2-methylacyl-CoA dehydrogenase | short-chain 2-methylacyl-CoA:electron-transfer flavoprotein 2-oxidoreductase | |
| 1.3.8.6 | glutaryl-CoA dehydrogenase (ETF) | glutaryl-CoA:electron-transfer flavoprotein 2,3-oxidoreductase (decarboxylating) | |
| 1.4.3.1 | D-aspartate oxidase | D-aspartate:oxygen oxidoreductase (deaminating) | |
| 1.4.3.2 | L-amino-acid oxidase | L-amino-acid:oxygen oxidoreductase (deaminating) | |
| 1.4.3.25 | L-arginine oxidase | L-arginine:oxygen oxidoreductase (deaminating) | |
| 1.4.3.3 | D-amino-acid oxidase | D-amino-acid:oxygen oxidoreductase (deaminating) | |
| 1.4.4.2 | glycine dehydrogenase (aminomethyl-transferring) | glycine:H-protein-lipoyllysine oxidoreductase (decarboxylating, acceptor-amino-methylating) | |
| 1.5.1.1 | 1-piperideine-2-carboxylate/1-pyrroline-2-carboxylate reductase [NAD(P)H] | L-pipecolate/L-proline:NAD(P)+ 2-oxidoreductase | |
| 1.5.1.2 | pyrroline-5-carboxylate reductase | L-proline:NAD(P)+ 5-oxidoreductase | |
| 1.5.1.25 | thiomorpholine-carboxylate dehydrogenase | thiomorpholine-3-carboxylate:NAD(P)+ 5,6-oxidoreductase | |
| 1.5.1.34 | 6,7-dihydropteridine reductase | 5,6,7,8-tetrahydropteridine:NAD(P)+ oxidoreductase | |
| 1.5.1.8 | saccharopine dehydrogenase (NADP+, L-lysine-forming) | N6-(L-1,3-dicarboxypropyl)-L-lysine:NADP+ oxidoreductase (L-lysine-forming) | |
| 1.5.1.9 | saccharopine dehydrogenase (NAD+, L-glutamate-forming) | N6-(L-1,3-dicarboxypropyl)-L-lysine:NAD+ oxidoreductase (L-glutamate-forming) | |
| 1.5.3.1 | sarcosine oxidase (formaldehyde-forming) | sarcosine:oxygen oxidoreductase (demethylating) | |
| 1.5.3.13 | N1-acetylpolyamine oxidase | N1-acetylpolyamine:oxygen oxidoreductase (3-acetamidopropanal-forming) | |
| 1.5.3.7 | L-pipecolate oxidase | L-pipecolate:oxygen 1,6-oxidoreductase | |
| 1.5.5.2 | proline dehydrogenase | L-proline:quinone oxidoreductase | |
| 1.5.5.3 | hydroxyproline dehydrogenase | trans-4-hydroxy-L-proline:quinone oxidoreductase | |
| 1.5.8.3 | sarcosine dehydrogenase | sarcosine, 5,6,7,8-tetrahydrofolate:electron-transferflavoprotein oxidoreductase (demethylating,5,10-methylenetetrahydrofolate-forming) | |
| 1.5.8.4 | dimethylglycine dehydrogenase | N,N-dimethylglycine,5,6,7,8-tetrahydrofolate:electron-transferflavoprotein oxidoreductase (demethylating,5,10-methylenetetrahydrofolate-forming) | |
| 1.6.3.1 | NAD(P)H oxidase (H2O2-forming) | NAD(P)H:oxygen oxidoreductase (H2O2-forming) | |
| 1.6.5.2 | NAD(P)H dehydrogenase (quinone) | NAD(P)H:quinone oxidoreductase | |
| 1.8.1.4 | dihydrolipoyl dehydrogenase | protein-N6-(dihydrolipoyl)lysine:NAD+ oxidoreductase | |
| 1.8.1.9 | thioredoxin-disulfide reductase | thioredoxin:NADP+ oxidoreductase | |
| 1.8.3.1 | sulfite oxidase | sulfite:oxygen oxidoreductase | |
| 1.8.5.8 | eukaryotic sulfide quinone oxidoreductase | sulfide:glutathione,quinone oxidoreductase | |
| 2.1.1.10 | homocysteine S-methyltransferase | S-adenosyl-L-methionine:L-homocysteine S-methyltransferase | |
| 2.1.1.13 | methionine synthase | 5-methyltetrahydrofolate:L-homocysteine S-methyltransferase | |
| 2.1.1.2 | guanidinoacetate N-methyltransferase | S-adenosyl-L-methionine:N-guanidinoacetate methyltransferase | |
| 2.1.1.20 | glycine N-methyltransferase | S-adenosyl-L-methionine:glycine N-methyltransferase | |
| 2.1.1.22 | carnosine N-methyltransferase | S-adenosyl-L-methionine:carnosine N-methyltransferase | |
| 2.1.1.28 | phenylethanolamine N-methyltransferase | S-adenosyl-L-methionine:phenylethanolamine N-methyltransferase | |
| 2.1.1.4 | acetylserotonin O-methyltransferase | S-adenosyl-L-methionine:N-acetylserotonin O-methyltransferase | |
| 2.1.1.49 | amine N-methyltransferase | S-adenosyl-L-methionine:amine N-methyltransferase | |
| 2.1.1.5 | betaine-homocysteine S-methyltransferase | trimethylammonioacetate:L-homocysteine S-methyltransferase | |
| 2.1.1.8 | histamine N-methyltransferase | S-adenosyl-L-methionine:histamine N-tele-methyltransferase | |
| 2.1.1.96 | thioether S-methyltransferase | S-adenosyl-L-methionine:dimethyl-sulfide S-methyltransferase | |
| 2.1.2.1 | glycine hydroxymethyltransferase | 5,10-methylenetetrahydrofolate:glycine hydroxymethyltransferase | |
| 2.1.2.10 | aminomethyltransferase | [protein]-S8-aminomethyldihydrolipoyllysine:tetrahydrofolate aminomethyltransferase (ammonia-forming) | |
| 2.1.2.5 | glutamate formimidoyltransferase | 5-formimidoyltetrahydrofolate:L-glutamate N-formimidoyltransferase | |
| 2.1.3.3 | ornithine carbamoyltransferase | carbamoyl-phosphate:L-ornithine carbamoyltransferase | |
| 2.1.4.1 | glycine amidinotransferase | L-arginine:glycine amidinotransferase | |
| 2.3.1.1 | amino-acid N-acetyltransferase | acetyl-CoA:L-glutamate N-acetyltransferase | |
| 2.3.1.168 | dihydrolipoyllysine-residue (2-methylpropanoyl)transferase | 2-methylpropanoyl-CoA:enzyme-N6-(dihydrolipoyl)lysine S-(2-methylpropanoyl)transferase | |
| 2.3.1.17 | aspartate N-acetyltransferase | acetyl-CoA:L-aspartate N-acetyltransferase | |
| 2.3.1.225 | protein S-acyltransferase | palmitoyl-CoA:[protein]-L-cysteine S-palmitoyltransferase | |
| 2.3.1.57 | diamine N-acetyltransferase | acetyl-CoA:alkane-alpha,omega-diamine N-acetyltransferase | |
| 2.3.1.61 | dihydrolipoyllysine-residue succinyltransferase | succinyl-CoA:enzyme-N6-(dihydrolipoyl)lysine S-succinyltransferase | |
| 2.3.1.87 | aralkylamine N-acetyltransferase | acetyl-CoA:2-arylethylamine N-acetyltransferase | |
| 2.3.1.9 | acetyl-CoA C-acetyltransferase | acetyl-CoA:acetyl-CoA C-acetyltransferase | |
| 2.4.2.28 | S-methyl-5'-thioadenosine phosphorylase | S-methyl-5'-thioadenosine:phosphate S-methyl-5-thio-alpha-D-ribosyl-transferase | |
| 2.5.1.16 | spermidine synthase | S-adenosyl 3-(methylthio)propylamine:putrescine 3-aminopropyltransferase | |
| 2.5.1.18 | glutathione transferase | RX:glutathione R-transferase | |
| 2.5.1.22 | spermine synthase | S-adenosyl 3-(methylthio)propylamine:spermidine 3-aminopropyltransferase | |
| 2.6.1.1 | aspartate transaminase | L-aspartate:2-oxoglutarate aminotransferase | |
| 2.6.1.13 | ornithine aminotransferase | L-ornithine:2-oxo-acid aminotransferase | |
| 2.6.1.18 | beta-alanine-pyruvate transaminase | L-alanine:3-oxopropanoate aminotransferase | |
| 2.6.1.2 | alanine transaminase | L-alanine:2-oxoglutarate aminotransferase | |
| 2.6.1.3 | cysteine transaminase | L-cysteine:2-oxoglutarate aminotransferase | |
| 2.6.1.39 | 2-aminoadipate transaminase | L-2-aminoadipate:2-oxoglutarate aminotransferase | |
| 2.6.1.4 | glycine transaminase | glycine:2-oxoglutarate aminotransferase | |
| 2.6.1.40 | (R)-3-amino-2-methylpropionate-pyruvate transaminase | (R)-3-amino-2-methylpropanoate:pyruvate aminotransferase | |
| 2.6.1.42 | branched-chain-amino-acid transaminase | branched-chain-amino-acid:2-oxoglutarate aminotransferase | |
| 2.6.1.44 | alanine-glyoxylate transaminase | L-alanine:glyoxylate aminotransferase | |
| 2.6.1.5 | tyrosine transaminase | L-tyrosine:2-oxoglutarate aminotransferase | |
| 2.6.1.51 | serine-pyruvate transaminase | L-serine:pyruvate aminotransferase | |
| 2.6.1.52 | phosphoserine transaminase | O-phospho-L-serine:2-oxoglutarate aminotransferase | |
| 2.6.1.63 | kynurenine-glyoxylate transaminase | L-kynurenine:glyoxylate aminotransferase (cyclizing) | |
| 2.6.1.64 | glutamine-phenylpyruvate transaminase | L-glutamine:phenylpyruvate aminotransferase | |
| 2.6.1.7 | kynurenine-oxoglutarate transaminase | L-kynurenine:2-oxoglutarate aminotransferase | |
| 2.6.1.73 | methionine-glyoxylate transaminase | L-methionine:glyoxylate aminotransferase | |
| 2.7.1.164 | O-phosphoseryl-tRNASec kinase | ATP:L-seryl-tRNASec O-phosphotransferase | |
| 2.7.1.81 | hydroxylysine kinase | GTP:5-hydroxy-L-lysine O-phosphotransferase | |
| 2.7.11.1 | non-specific serine/threonine protein kinase | ATP:protein phosphotransferase (non-specific) | |
| 2.7.11.4 | [3-methyl-2-oxobutanoate dehydrogenase (acetyl-transferring)] kinase | ATP:[3-methyl-2-oxobutanoate dehydrogenase (acetyl-transferring)] phosphotransferase | |
| 2.7.3.2 | creatine kinase | ATP:creatine N-phosphotransferase | |
| 2.7.9.3 | selenide, water dikinase | ATP:selenide, water phosphotransferase | |
| 2.8.1.1 | thiosulfate sulfurtransferase | thiosulfate:cyanide sulfurtransferase | |
| 2.8.1.2 | 3-mercaptopyruvate sulfurtransferase | 3-mercaptopyruvate:cyanide sulfurtransferase | |
| 2.8.1.3 | thiosulfate-thiol sulfurtransferase | thiosulfate:thiol sulfurtransferase | |
| 2.9.1.2 | O-phospho-L-seryl-tRNASec:L-selenocysteinyl-tRNA synthase | selenophosphate:O-phospho-L-seryl-tRNASec selenium transferase | |
| 3.1.1.47 | 1-alkyl-2-acetylglycerophosphocholine esterase | 1-alkyl-2-acetyl-sn-glycero-3-phosphocholine acetohydrolase | |
| 3.1.1.5 | lysophospholipase | 2-lysophosphatidylcholine acylhydrolase | |
| 3.1.2.4 | 3-hydroxyisobutyryl-CoA hydrolase | 3-hydroxy-2-methylpropanoyl-CoA hydrolase | |
| 3.1.3.16 | protein-serine/threonine phosphatase | protein-serine/threonine-phosphate phosphohydrolase | |
| 3.1.3.3 | phosphoserine phosphatase | O-phosphoserine phosphohydrolase | |
| 3.1.3.52 | [3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)]-phosphatase | [3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)]-phosphate phosphohydrolase | |
| 3.1.3.77 | acireductone synthase | 5-(methylthio)-2,3-dioxopentyl-phosphate phosphohydrolase (isomerizing) | |
| 3.13.2.1 | adenosylhomocysteinase | S-adenosyl-L-homocysteine hydrolase | |
| 3.4.19.5 | beta-aspartyl-peptidase | ||
| 3.5.1.1 | asparaginase | L-asparagine amidohydrolase | |
| 3.5.1.15 | aspartoacylase | N-acyl-L-aspartate amidohydrolase | |
| 3.5.1.2 | glutaminase | L-glutamine amidohydrolase | |
| 3.5.1.9 | arylformamidase | aryl-formylamine amidohydrolase | |
| 3.5.2.7 | imidazolonepropionase | 3-(5-oxo-4,5-dihydro-3H-imidazol-4-yl)propanoate amidohydrolase | |
| 3.5.3.1 | arginase | L-arginine amidinohydrolase | |
| 3.5.3.17 | Guanidinopropionase | 3-Guanidinopropanoate amidinopropionase | |
| 3.5.3.7 | guanidinobutyrase | 4-guanidinobutanoate amidinohydrolase | |
| 3.5.99.10 | 2-iminobutanoate/2-iminopropanoate deaminase | 2-iminobutanoate aminohydrolase | |
| 3.7.1.2 | fumarylacetoacetase | 4-fumarylacetoacetate fumarylhydrolase | |
| 3.7.1.3 | kynureninase | L-kynurenine hydrolase | |
| 4.1.1.11 | aspartate 1-decarboxylase | L-aspartate 1-carboxy-lyase (beta-alanine-forming) | |
| 4.1.1.17 | ornithine decarboxylase | L-ornithine carboxy-lyase (putrescine-forming) | |
| 4.1.1.22 | histidine decarboxylase | L-histidine carboxy-lyase (histamine-forming) | |
| 4.1.1.28 | aromatic-L-amino-acid decarboxylase | Aromatic-L-amino-acid carboxy-lyase | |
| 4.1.1.29 | sulfinoalanine decarboxylase | 3-sulfino-L-alanine carboxy-lyase (hypotaurine-forming) | |
| 4.1.1.45 | aminocarboxymuconate-semialdehyde decarboxylase | 2-amino-3-(3-oxoprop-1-en-1-yl)but-2-enedioate carboxy-lyase (2-aminomuconate-semialdehyde-forming) | |
| 4.1.1.50 | adenosylmethionine decarboxylase | S-adenosyl-L-methionine carboxy-lyase [(5-deoxy-5-adenosyl)(3-aminopropyl)methylsulfonium-salt-forming] | |
| 4.1.3.16 | 4-Hydroxy-2-oxoglutarate aldolase | 4-hydroxy-2-oxoglutarate glyoxylate-lyase (pyruvate-forming) | |
| 4.2.1.109 | methylthioribulose 1-phosphate dehydratase | S-methyl-5-thio-D-ribulose-1-phosphate 4-hydro-lyase [5-(methylthio)-2,3-dioxopentyl-phosphate-forming] | |
| 4.2.1.17 | enoyl-CoA hydratase | (3S)-3-hydroxyacyl-CoA hydro-lyase | |
| 4.2.1.18 | methylglutaconyl-CoA hydratase | (S)-3-hydroxy-3-methylglutaryl-CoA hydro-lyase (trans-3-methylglutaconyl-CoA-forming) | |
| 4.2.1.22 | cystathionine beta-synthase | L-serine hydro-lyase (adding homocysteine; L-cystathionine-forming) | |
| 4.2.1.49 | urocanate hydratase | 3-(5-oxo-4,5-dihydro-3H-imidazol-4-yl)propanoate hydro-lyase (urocanate-forming) | |
| 4.2.1.56 | itaconyl-CoA hydratase | citramalyl-CoA hydro-lyase (itaconyl-CoA-forming) | |
| 4.2.1.96 | 4a-hydroxytetrahydrobiopterin dehydratase | 4a-hydroxytetrahydrobiopterin hydro-lyase (6,7-dihydrobiopterin-forming) | |
| 4.2.3.134 | 5-phosphooxy-L-lysine phospho-lyase | (5R)-5-phosphonooxy-L-lysine phosphate-lyase (deaminating; (S)-2-amino-6-oxohexanoate-forming) | |
| 4.3.1.17 | L-serine ammonia-lyase | L-serine ammonia-lyase (pyruvate-forming) | |
| 4.3.1.18 | D-Serine ammonia-lyase | D-serine ammonia-lyase (pyruvate-forming) | |
| 4.3.1.19 | threonine ammonia-lyase | L-threonine ammonia-lyase (2-oxobutanoate-forming) | |
| 4.3.1.3 | histidine ammonia-lyase | L-histidine ammonia-lyase (urocanate-forming) | |
| 4.3.1.4 | formimidoyltetrahydrofolate cyclodeaminase | 5-formimidoyltetrahydrofolate ammonia-lyase (cyclizing; 5,10-methenyltetrahydrofolate-forming) | |
| 4.3.2.1 | argininosuccinate lyase | 2-(Nomega-L-arginino)succinate arginine-lyase (fumarate-forming) | |
| 4.4.1.1 | cystathionine gamma-lyase | L-cystathionine cysteine-lyase (deaminating; 2-oxobutanoate-forming) | |
| 4.4.1.13 | cysteine-S-conjugate beta-lyase | L-cysteine-S-conjugate thiol-lyase (deaminating; pyruvate-forming) | |
| 4.4.1.16 | selenocysteine lyase | L-selenocysteine selenide-lyase (L-alanine-forming) | |
| 4.4.1.2 | homocysteine desulfhydrase | L-homocysteine hydrogen-sulfide-lyase (deaminating; 2-oxobutanoate-forming) | |
| 5.1.1.18 | serine racemase | serine racemase | |
| 5.1.1.3 | glutamate racemase | glutamate racemase | |
| 5.2.1.2 | maleylacetoacetate isomerase | 4-maleylacetoacetate cis-trans-isomerase | |
| 5.3.1.23 | S-methyl-5-thioribose-1-phosphate isomerase | S-methyl-5-thio-alpha-D-ribose-1-phosphate aldose-ketose-isomerase | |
| 5.3.3.12 | L-dopachrome isomerase | L-dopachrome keto-enol isomerase | |
| 5.3.3.8 | DELTA3-DELTA2-enoyl-CoA isomerase | (3Z/3E)-alk-3-enoyl-CoA (2E)-isomerase | |
| 6.1.1.10 | methionine-tRNA ligase | L-methionine:tRNAMet ligase (AMP-forming) | |
| 6.1.1.11 | serine-tRNA ligase | L-serine:tRNASer ligase (AMP-forming) | |
| 6.1.1.12 | aspartate-tRNA ligase | L-aspartate:tRNAAsp ligase (AMP-forming) | |
| 6.1.1.15 | proline-tRNA ligase | L-proline:tRNAPro ligase (AMP-forming) | |
| 6.1.1.17 | glutamate-tRNA ligase | L-glutamate:tRNAGlu ligase (AMP-forming) | |
| 6.1.1.18 | glutamine-tRNA ligase | L-glutamine:tRNAGln ligase (AMP-forming) | |
| 6.1.1.19 | arginine-tRNA ligase | L-arginine:tRNAArg ligase (AMP-forming) | |
| 6.1.1.4 | leucine-tRNA ligase | L-leucine:tRNALeu ligase (AMP-forming) | |
| 6.1.1.5 | isoleucine-tRNA ligase | L-isoleucine:tRNAIle ligase (AMP-forming) | |
| 6.1.1.6 | lysine-tRNA ligase | L-lysine:tRNALys ligase (AMP-forming) | |
| 6.3.1.2 | glutamine synthetase | L-glutamate:ammonia ligase (ADP-forming) | |
| 6.3.2.11 | carnosine synthase | L-histidine:beta-alanine ligase (ADP-forming) | |
| 6.3.4.16 | carbamoyl-phosphate synthase (ammonia) | carbon-dioxide:ammonia ligase (ADP-forming, carbamate-phosphorylating) | |
| 6.3.4.5 | argininosuccinate synthase | L-citrulline:L-aspartate ligase (AMP-forming) | |
| 6.3.5.4 | asparagine synthase (glutamine-hydrolysing) | L-aspartate:L-glutamine amido-ligase (AMP-forming) | |
| 6.4.1.4 | methylcrotonoyl-CoA carboxylase | 3-methylcrotonoyl-CoA:carbon-dioxide ligase (ADP-forming) |
Proteins
| Protein ID | name | full name |
|---|