| BioCyc:HUMAN_ILEUDEG-PWY |
isoleucine degradation |
| BioCyc:HUMAN_PWY-5328 |
superpathway of methionine degradation |
| BioCyc:META_ILEUDEG-PWY |
L-isoleucine degradation I |
| BioCyc:META_PWY-5328 |
superpathway of L-methionine salvage and degradation |
| BioCyc:MTBH37RV_PWY-5046 |
2-oxoisovalerate decarboxylation to isobutanoyl-CoA |
| BioCyc:HUMAN_PWY-5046 |
2-oxoisovalerate decarboxylation to isobutanoyl-CoA |
| BioCyc:HUMAN_LEU-DEG2-PWY |
leucine degradation |
| BioCyc:META_PWY-5046 |
2-oxoisovalerate decarboxylation to isobutanoyl-CoA |
| BioCyc:META_PWY-5130 |
2-oxobutanoate degradation I |
| BioCyc:META_PWY66-428 |
L-threonine degradation V |
| BioCyc:META_VALDEG-PWY |
L-valine degradation I |
| BioCyc:MOUSE_PWY3DJ-0 |
isoleucine degradation |
| BioCyc:MOUSE_PWY3DJ-6 |
Leucine Catabolism |
| BioCyc:BSUB_VALDEG-PWY |
L-valine degradation I |
| BioCyc:BSUB_PYRUVDEHYD-PWY |
pyruvate decarboxylation to acetyl CoA |
| BioCyc:HUMAN_PWY66-428 |
threonine degradation |
| BioCyc:HUMAN_VALDEG-PWY |
valine degradation |
| BioCyc:MOUSE_PWY-5046 |
branched-chain α-keto acid dehydrogenase complex |
| BioCyc:BSUB_ILEUDEG-PWY |
L-isoleucine degradation I |
| BioCyc:BSUB_PWY-5130 |
2-oxobutanoate degradation I |
| BioCyc:HUMAN_PWY-5130 |
2-oxobutanoate degradation |
| BioCyc:META_LEU-DEG2-PWY |
L-leucine degradation I |
| BioCyc:MTBH37RV_VALDEG-PWY |
L-valine degradation I |
| BioCyc:MOUSE_PWY3DJ-86 |
valine degradation |
| BioCyc:BSUB_PWY-5046 |
2-oxoisovalerate decarboxylation to isobutanoyl-CoA |
| Reactome:R-HSA-9865118 |
Diseases of branched-chain amino acid catabolism |
| Reactome:R-HSA-9907570 |
Loss-of-function mutations in DLD cause MSUD3/DLDD |
| Reactome:R-BTA-9859138 |
BCKDH synthesizes BCAA-CoA from KIC, KMVA, KIV |
| Reactome:R-CEL-9859138 |
BCKDH synthesizes BCAA-CoA from KIC, KMVA, KIV |
| Reactome:R-HSA-9859138 |
BCKDH synthesizes BCAA-CoA from KIC, KMVA, KIV |
| Reactome:R-HSA-9865114 |
Maple Syrup Urine Disease |
| Reactome:R-HSA-9912529 |
H139Hfs13* PPM1K causes a mild variant of MSUD |
| Reactome:R-HSA-9865125 |
Loss-of-function mutations in BCKDHA or BCKDHB cause MSUD |
| Reactome:R-HSA-9912481 |
Branched-chain ketoacid dehydrogenase kinase deficiency |
| Reactome:R-MMU-9859138 |
BCKDH synthesizes BCAA-CoA from KIC, KMVA, KIV |
| Reactome:R-BTA-1430728 |
Metabolism |
| Reactome:R-BTA-71291 |
Amino acid and derivative metabolism |
| Reactome:R-CEL-70895 |
Branched-chain amino acid catabolism |
| Reactome:R-HSA-70895 |
Branched-chain amino acid catabolism |
| Reactome:R-HSA-1643685 |
Disease |
| Reactome:R-MMU-1430728 |
Metabolism |
| Reactome:R-MMU-70895 |
Branched-chain amino acid catabolism |
| Reactome:R-BTA-70895 |
Branched-chain amino acid catabolism |
| Reactome:R-CEL-71291 |
Amino acid and derivative metabolism |
| Reactome:R-HSA-71291 |
Amino acid and derivative metabolism |
| Reactome:R-HSA-5668914 |
Diseases of metabolism |
| Reactome:R-MMU-71291 |
Amino acid and derivative metabolism |
| Reactome:R-CEL-1430728 |
Metabolism |
| Reactome:R-HSA-1430728 |
Metabolism |
| WikiPathways:WP4686 |
Leucine, isoleucine and valine metabolism |
| PathBank:SMP0000032 |
Valine, Leucine, and Isoleucine Degradation |
| PathBank:SMP0000016 |
Propanoate Metabolism |
| PathBank:SMP0000173 |
beta-Ketothiolase Deficiency |
| PathBank:SMP0000199 |
Maple Syrup Urine Disease |
| PathBank:SMP0000384 |
Methylmalonate Semialdehyde Dehydrogenase Deficiency |
| PathBank:SMP0000141 |
3-Methylglutaconic Aciduria Type IV |
| PathBank:SMP0000524 |
Isovaleric Acidemia |
| PathBank:SMP0002433 |
Leucine Degradation |
| PathBank:SMP0000138 |
3-Hydroxy-3-methylglutaryl-CoA Lyase Deficiency |
| PathBank:SMP0000140 |
3-Methylglutaconic Aciduria Type III |
| PathBank:SMP0000238 |
Isovaleric Aciduria |
| PathBank:SMP0000201 |
Methylmalonic Aciduria Due to Cobalamin-Related Disorders |
| PathBank:SMP0000523 |
Isobutyryl-CoA Dehydrogenase Deficiency |
| PathBank:SMP0000137 |
2-Methyl-3-hydroxybutyryl-CoA Dehydrogenase Deficiency |
| PathBank:SMP0000237 |
3-Methylcrotonyl-CoA Carboxylase Deficiency Type I |
| PathBank:SMP0000200 |
Methylmalonic Aciduria |
| PathBank:SMP0000521 |
3-Hydroxyisobutyric Acid Dehydrogenase Deficiency |
| PathBank:SMP0002460 |
Valine Degradation |
| PathBank:SMP0087480 |
Propanoate Metabolism |
| PathBank:SMP0087516 |
Threonine and 2-Oxobutanoate Degradation |
| PathBank:SMP0000452 |
Threonine and 2-Oxobutanoate Degradation |
| PathBank:SMP0000236 |
Propionic Acidemia |
| PathBank:SMP0000139 |
3-Methylglutaconic Aciduria Type I |
| PathBank:SMP0000198 |
Malonic Aciduria |
| PathBank:SMP0000502 |
Malonyl-CoA Decarboxylase Deficiency |
| PathBank:SMP0000522 |
3-Hydroxyisobutyric Aciduria |
| PathBank:SMP0002431 |
Isoleucine Degradation |