EC: 2.4.1.11

glycogen(starch) synthase (UDP-glucose:glycogen 4-alpha-D-glucosyltransferase)

enzyme lambda metabolic reaction experiment
- [glycogen(starch) synthase(Enzyme) wildtype D form]

(1,4_alpha_D_Glucosyl)n + UDPglucose -> UDP + (1,4_alpha_D_Glucosyl)n
(( (V * S) ) / (Km + S)) buffer: 10 mM K2HPO4/KH2PO4, 20 mM imidazole-HCl, 150 mM KCl, 5 mM MgCl2
PH: 7.2
Temperature: 38
- [glycogen(starch) synthase(Enzyme) wildtype I form]

UDPglucose + (1,4_alpha_D_Glucosyl)n -> (1,4_alpha_D_Glucosyl)n + UDP
(( (V * S) ) / (Km + S)) buffer: 10 mM K2HPO4/KH2PO4, 20 mM imidazole-HCl, 150 mM KCl, 5 mM MgCl2
PH: 7.2
Temperature: 38

Pathways

pathway id name
Reactome:R-BTA-1430728 Metabolism
Reactome:R-CEL-8982491 Glycogen metabolism
Reactome:R-DME-71387 Carbohydrate metabolism
Reactome:R-HSA-8982491 Glycogen metabolism
Reactome:R-HSA-1643685 Disease
Reactome:R-HSA-3828062 GSD 0 (muscle)
Reactome:R-MMU-1430728 Metabolism
Reactome:R-RNO-3322077 Glycogen synthesis
Reactome:R-SCE-71387 Carbohydrate metabolism
Reactome:R-BTA-3322077 Glycogen synthesis
Reactome:R-CEL-71387 Carbohydrate metabolism
Reactome:R-DME-1430728 Metabolism
Reactome:R-HSA-71387 Carbohydrate metabolism
Reactome:R-HSA-3229121 Glycogen storage diseases
Reactome:R-HSA-3785653 Myoclonic epilepsy of Lafora
Reactome:R-MMU-3322077 Glycogen synthesis
Reactome:R-RNO-8982491 Glycogen metabolism
Reactome:R-SCE-1430728 Metabolism
Reactome:R-BTA-71387 Carbohydrate metabolism
Reactome:R-CEL-3322077 Glycogen synthesis
Reactome:R-DME-8982491 Glycogen metabolism
Reactome:R-HSA-3322077 Glycogen synthesis
Reactome:R-HSA-5668914 Diseases of metabolism
Reactome:R-HSA-3878781 GSD IV
Reactome:R-MMU-71387 Carbohydrate metabolism
Reactome:R-RNO-1430728 Metabolism
Reactome:R-SCE-8982491 Glycogen metabolism
Reactome:R-BTA-8982491 Glycogen metabolism
Reactome:R-CEL-1430728 Metabolism
Reactome:R-DME-3322077 Glycogen synthesis
Reactome:R-HSA-1430728 Metabolism
Reactome:R-HSA-5663084 Diseases of carbohydrate metabolism
Reactome:R-HSA-3814836 GSD XV
Reactome:R-MMU-8982491 Glycogen metabolism
Reactome:R-RNO-71387 Carbohydrate metabolism
Reactome:R-SCE-3322077 Glycogen synthesis
PathBank:SMP0000552 Glycogen Synthetase Deficiency
PathBank:SMP0000556 Mucopolysaccharidosis VII. Sly Syndrome
PathBank:SMP0000555 Glycogenosis, Type VI. Hers Disease
PathBank:SMP0000553 Glycogenosis, Type III. Cori Disease, Debrancher Glycogenosis
PathBank:SMP0000557 Sucrase-Isomaltase Deficiency
PathBank:SMP0087252 Starch and Sucrose Metabolism
PathBank:SMP0000058 Starch and Sucrose Metabolism
PathBank:SMP0000554 Glycogenosis, Type IV. Amylopectinosis, Anderson Disease
PathBank:SMP0002380 Starch and Sucrose Metabolism