D-galactose degradation I (Leloir pathway)
Frey PA. The Leloir pathway: a mechanistic imperative for three enzymes to change the stereochemical configuration of a single carbon in galactose. The FASEB Journal. 1996 Mar;10(4):461–70. doi: 10.1096/fasebj.10.4.8647345.
Metabolites
Enzyme
| EC Number | name | full name | note |
|---|---|---|---|
| 2.7.1.6 | galactokinase | ATP:D-galactose 1-phosphotransferase | |
| 2.7.7.12 | UDP-glucose-hexose-1-phosphate uridylyltransferase | UDP-glucose:alpha-D-galactose-1-phosphate uridylyltransferase | |
| 5.1.3.2 | UDP-glucose 4-epimerase | UDP-glucose 4-epimerase | |
| 5.1.3.3 | Aldose 1-epimerase | Aldose 1-epimerase | |
| 5.1.3.5 | UDP-arabinose 4-epimerase | UDP-L-arabinose 4-epimerase | |
| 5.4.2.2 | phosphoglucomutase (alpha-D-glucose-1,6-bisphosphate-dependent) | alpha-D-glucose 1,6-phosphomutase |
Proteins
| Protein ID | name | full name |
|---|---|---|
| P09147 | galE | UDP-glucose 4-epimerase |
| P09148 | galT | Galactose-1-phosphate uridylyltransferase |
| P0A6T3 | galK | Galactokinase |
| P0A9C3 | galM | Aldose 1-epimerase |
| P21955 | galM | Aldose 1-epimerase |
| P21977 | galE | UDP-glucose 4-epimerase |
| P36938 | pgm | Phosphoglucomutase |