Sulfite Oxidase Deficiency

Metabolites

ADP

Formula: C10H15N5O10P2 (427.02941500000003)

CAS ID: 58-64-0

Aryl sulfate

Formula: C6H6O4S (173.9986796)

CAS ID: 937-34-8

ATP

Formula: C10H16N5O13P3 (506.9957476)

CAS ID: 56-65-5

Estrone

Formula: C18H22O2 (270.1619712)

CAS ID: 53-16-7

Estrone 3-sulfate

Formula: C18H22O5S (350.11878820000004)

CAS ID: 481-97-0

H2O

Formula: H2O (18.0105642)

CAS ID: 7732-18-5

Hydrogen peroxide

Formula: H2O2 (34.0054792)

CAS ID: 7722-84-1

Oxygen

Formula: O2 (31.98983)

CAS ID: 7782-44-7

Propane-1-ol

Formula: C3H8O (60.0575118)

CAS ID: 71-23-8

Sulfate

Formula: H2SO4 (97.9673812)

CAS ID: 7664-93-9

diphosphate

Formula: O7P2 (173.911931)

CAS ID: 14000-31-8

phosphate(3-)

Formula: O4P (94.953423)

CAS ID: 14265-44-2

sulfite

Formula: O3S (79.956817)

CAS ID: 14265-45-3

Chondroitin

Formula: C14H21NO11 (379.1114556)

CAS ID: 9007-27-6



Enzyme

EC Number name full name note
1.8.3.1 sulfite oxidase sulfite:oxygen oxidoreductase
2.7.1.25 adenylyl-sulfate kinase ATP:adenylyl-sulfate 3'-phosphotransferase
2.7.7.4 sulfate adenylyltransferase ATP:sulfate adenylyltransferase
2.8.2.1 aryl sulfotransferase 3'-phosphoadenylyl-sulfate:phenol sulfotransferase
2.8.2.2 alcohol sulfotransferase 3'-phosphoadenylyl-sulfate:alcohol sulfotransferase
2.8.2.5 chondroitin 4-sulfotransferase 3'-phosphoadenylyl-sulfate:chondroitin 4'-sulfotransferase
3.1.3.57 inositol-1,4-bisphosphate 1-phosphatase 1D-myo-inositol-1,4-bisphosphate 1-phosphohydrolase
3.1.3.7 3'(2'),5'-bisphosphate nucleotidase adenosine-3'(2'),5'-bisphosphate 3'(2')-phosphohydrolase


Proteins

Protein ID name full name