Glucose-6-phosphate Dehydrogenase Deficiency

Metabolites

2-Deoxy-D-ribose 1-phosphate

Formula: C5H11O7P (214.0242386)

CAS ID: 17210-42-3

2-Deoxy-D-ribose 5-phosphate

Formula: C5H11O7P (214.0242386)

CAS ID: 102916-66-5

6-Phospho-D-gluconate

Formula: C6H13O10P (276.0246328)

CAS ID: 921-62-0

Acetaldehyde

Formula: C2H4O (44.0262134)

CAS ID: 75-07-0

ADP

Formula: C10H15N5O10P2 (427.02941500000003)

CAS ID: 58-64-0

alpha-D-Ribose 1-phosphate

Formula: C5H11O8P (230.0191536)

CAS ID: 14075-00-4

AMP

Formula: C10H14N5O7P (347.06308240000004)

CAS ID: 61-19-8

ATP

Formula: C10H16N5O13P3 (506.9957476)

CAS ID: 56-65-5

beta-D-Glucose 6-phosphate

Formula: C6H13O9P (260.0297178)

CAS ID: 15209-12-8

CO2

Formula: CO2 (43.98983)

CAS ID: 124-38-9

D-Fructose 6-phosphate

Formula: C6H13O9P (260.0297178)

CAS ID: 643-13-0

D-Glucose 6-phosphate

Formula: C6H13O9P (260.0297178)

CAS ID: 56-73-5

D-Ribose

Formula: C5H10O5 (150.052821)

CAS ID: 50-69-1

D-Ribose 5-phosphate

Formula: C5H11O8P (230.0191536)

CAS ID: 4300-28-1

D-Ribulose 5-phosphate

Formula: C5H11O8P (230.0191536)

CAS ID: 551-85-9

D-Xylulose 5-phosphate

Formula: C5H11O8P (230.0191536)

CAS ID: 4212-65-1

Glyceraldehyde 3-phosphate

Formula: C3H7O6P (169.9980252)

CAS ID: 591-59-3

Glycerone phosphate

Formula: C3H7O6P (169.9980252)

CAS ID: 57-04-5

H2O

Formula: H2O (18.0105642)

CAS ID: 7732-18-5

NADP+

Formula: C21H29N7O17P3 (744.0832754)

CAS ID: 53-59-8

Fructose-1,6-diphosphate

Formula: C6H14O12P2 (339.9960504)

CAS ID: 34693-23-7

phosphate(3-)

Formula: O4P (94.953423)

CAS ID: 14265-44-2



Enzyme

EC Number name full name note
1.-.-.-
1.1.1.44 phosphogluconate dehydrogenase (NADP+-dependent, decarboxylating) 6-phospho-D-gluconate:NADP+ 2-oxidoreductase (decarboxylating)
1.1.1.49 glucose-6-phosphate dehydrogenase (NADP+) D-glucose-6-phosphate:NADP+ 1-oxidoreductase
2.2.1.1 transketolase sedoheptulose-7-phosphate:D-glyceraldehyde-3-phosphate glycolaldehydetransferase
2.2.1.2 transaldolase sedoheptulose-7-phosphate:D-glyceraldehyde-3-phosphate glyceronetransferase
2.7.1.11 6-phosphofructokinase ATP:D-fructose-6-phosphate 1-phosphotransferase
2.7.1.15 ribokinase ATP:D-ribose 5-phosphotransferase
2.7.6.1 ribose-phosphate diphosphokinase ATP:D-ribose-5-phosphate diphosphotransferase
3.1.1.31 6-phosphogluconolactonase 6-phospho-D-glucono-1,5-lactone lactonohydrolase
3.1.3.11 fructose-bisphosphatase D-fructose-1,6-bisphosphate 1-phosphohydrolase
4.1.2.13 fructose-bisphosphate aldolase D-fructose-1,6-bisphosphate D-glyceraldehyde-3-phosphate-lyase (glycerone-phosphate-forming)
4.1.2.4 deoxyribose-phosphate aldolase 2-deoxy-D-ribose-5-phosphate acetaldehyde-lyase (D-glyceraldehyde-3-phosphate-forming)
5.1.3.1 ribulose-phosphate 3-epimerase D-ribulose-5-phosphate 3-epimerase
5.3.1.6 ribose-5-phosphate isomerase D-ribose-5-phosphate aldose-ketose-isomerase
5.3.1.9 glucose-6-phosphate isomerase alpha-D-glucose-6-phosphate aldose-ketose-isomerase (configuration-inverting)
5.4.2.2 phosphoglucomutase (alpha-D-glucose-1,6-bisphosphate-dependent) alpha-D-glucose 1,6-phosphomutase


Proteins

Protein ID name full name