Fructose Intolerance, Hereditary

Metabolites

ADP

Formula: C10H15N5O10P2 (427.02941500000003)

CAS ID: 58-64-0

alpha-D-Glucose

Formula: C6H12O6 (180.0633852)

CAS ID: 492-62-6

ATP

Formula: C10H16N5O13P3 (506.9957476)

CAS ID: 56-65-5

beta-D-Fructose

Formula: C6H12O6 (180.0633852)

CAS ID: 53188-23-1

beta-D-Fructose 2-phosphate

Formula: C6H13O9P (260.0297178)

CAS ID: 19046-69-6

D-Fructose 1-phosphate

Formula: C6H13O9P (260.0297178)

CAS ID: 15978-08-2

D-Fructose 6-phosphate

Formula: C6H13O9P (260.0297178)

CAS ID: 643-13-0

D-Mannose

Formula: C6H12O6 (180.0633852)

CAS ID: 3458-28-4

D-Mannose 6-phosphate

Formula: C6H13O9P (260.0297178)

CAS ID: 3672-15-9

D-Sorbitol

Formula: C6H14O6 (182.0790344)

CAS ID: 50-70-4

GDP-L-fucose

Formula: C16H25N5O15P2 (589.0822360000001)

CAS ID: 15839-70-0

GDP-mannose

Formula: C16H25N5O16P2 (605.0771510000001)

CAS ID: 3123-67-9

Glyceraldehyde

Formula: C3H6O3 (90.0316926)

CAS ID: 367-47-5

Glyceraldehyde 3-phosphate

Formula: C3H7O6P (169.9980252)

CAS ID: 591-59-3

Glycerone phosphate

Formula: C3H7O6P (169.9980252)

CAS ID: 57-04-5

GTP

Formula: C10H16N5O14P3 (522.9906626)

CAS ID: 86-01-1

H2O

Formula: H2O (18.0105642)

CAS ID: 7732-18-5

NAD+

Formula: C21H28N7O14P2 (664.1169428000001)

CAS ID: 53-84-9

NADH

Formula: C21H29N7O14P2 (665.1247674)

CAS ID: 58-68-4

NADP+

Formula: C21H29N7O17P3 (744.0832754)

CAS ID: 53-59-8

Orthophosphate

Formula: H3PO4 (97.9768968)

CAS ID: 7664-38-2

Fructose-1,6-diphosphate

Formula: C6H14O12P2 (339.9960504)

CAS ID: 34693-23-7

diphosphate

Formula: O7P2 (173.911931)

CAS ID: 14000-31-8

phosphate(3-)

Formula: O4P (94.953423)

CAS ID: 14265-44-2



Enzyme

EC Number name full name note
2.7.1.1 hexokinase ATP:D-hexose 6-phosphotransferase
2.7.1.11 6-phosphofructokinase ATP:D-fructose-6-phosphate 1-phosphotransferase
4.1.2.13 fructose-bisphosphate aldolase D-fructose-1,6-bisphosphate D-glyceraldehyde-3-phosphate-lyase (glycerone-phosphate-forming)
4.2.3.3 methylglyoxal synthase glycerone-phosphate phosphate-lyase (methylglyoxal-forming)
5.3.1.1 triose-phosphate isomerase D-glyceraldehyde-3-phosphate aldose-ketose-isomerase


Proteins

Protein ID name full name