Vitamin B6-dependent and responsive disorders

Metabolites

6-Amino-2-oxohexanoate

Formula: C6H11NO3 (145.0738896)

CAS ID: 10606-14-1

L-Lysine

Formula: C6H14N2O2 (146.1055224)

CAS ID: 56-87-1

L-Proline

Formula: C5H9NO2 (115.0633254)

CAS ID: 147-85-3

Pyridoxal

Formula: C8H9NO3 (167.0582404)

CAS ID: 66-72-8

Pyridoxal phosphate

Formula: C8H10NO6P (247.024573)

CAS ID: 54-47-7

Pyridoxine

Formula: C8H11NO3 (169.0738896)

CAS ID: 65-23-6

Pyridoxine phosphate

Formula: C8H12NO6P (249.0402222)

CAS ID: 447-05-2

L-2-Amino-6-oxohexanoic acid

Formula: C6H11NO3 (145.0738896)

CAS ID: 1962-83-0



Enzyme

EC Number name full name note
2.7.1.35 pyridoxal kinase ATP:pyridoxal 5'-phosphotransferase


Proteins

Protein ID name full name