Urea cycle
Metabolites
Enzyme
| EC Number | name | full name | note |
|---|---|---|---|
| 1.2.1.38 | N-acetyl-gamma-glutamyl-phosphate reductase | N-acetyl-L-glutamate-5-semialdehyde:NADP+ 5-oxidoreductase (phosphorylating) | |
| 2.1.3.3 | ornithine carbamoyltransferase | carbamoyl-phosphate:L-ornithine carbamoyltransferase | |
| 2.7.2.8 | acetylglutamate kinase | ATP:N-acetyl-L-glutamate 5-phosphotransferase | |
| 3.5.3.1 | arginase | L-arginine amidinohydrolase | |
| 4.3.2.1 | argininosuccinate lyase | 2-(Nomega-L-arginino)succinate arginine-lyase (fumarate-forming) | |
| 6.3.4.16 | carbamoyl-phosphate synthase (ammonia) | carbon-dioxide:ammonia ligase (ADP-forming, carbamate-phosphorylating) | |
| 6.3.5.5 | carbamoyl-phosphate synthase (glutamine-hydrolysing) | hydrogen-carbonate:L-glutamine amido-ligase (ADP-forming, carbamate-phosphorylating) |
Proteins
| Protein ID | name | full name |
|---|---|---|
| P00812 | CAR1 | Arginase |
| P03965 | CPA2 | Carbamoyl phosphate synthase arginine-specific large chain |
| P04076 | ARG4 | Argininosuccinate lyase |
| P05150 | ARG3 | Ornithine carbamoyltransferase |
| Q01217 | ARG5,6 | Protein ARG5,6, mitochondrial |