Succinyl CoA: 3-Ketoacid CoA Transferase Deficiency
Metabolites
Enzyme
| EC Number | name | full name | note |
|---|---|---|---|
| 1.1.1.146 | 11beta-hydroxysteroid dehydrogenase | 11beta-hydroxysteroid:NADP+ 11-oxidoreductase | |
| 1.1.1.201 | 7beta-hydroxysteroid dehydrogenase (NADP+) | 7beta-hydroxysteroid:NADP+ 7-oxidoreductase | |
| 2.3.3.10 | hydroxymethylglutaryl-CoA synthase | acetyl-CoA:acetoacetyl-CoA C-acetyltransferase (thioester-hydrolysing, carboxymethyl-forming) | |
| 2.8.3.5 | 3-oxoacid CoA-transferase | succinyl-CoA:3-oxo-acid CoA-transferase | |
| 4.1.3.4 | hydroxymethylglutaryl-CoA lyase | (S)-3-hydroxy-3-methylglutaryl-CoA acetoacetate-lyase (acetyl-CoA-forming) |
Proteins
| Protein ID | name | full name |
|---|