Urea cycle and metabolism of amino groups

Metabolites

(S)-1-Pyrroline-5-carboxylate

Formula: C5H7NO2 (113.0476762)

CAS ID: 64199-88-8

Ammonia

Formula: NH3 (17.0265478)

CAS ID: 7664-41-7

Carbamoyl phosphate

Formula: CH4NO5P (140.9827104)

CAS ID: 590-55-6

CO2

Formula: CO2 (43.98983)

CAS ID: 124-38-9

Formate

Formula: CH2O2 (46.0054792)

CAS ID: 64-18-6

Fumarate

Formula: C4H4O4 (116.01095839999999)

CAS ID: 110-17-8

Guanidinoacetate

Formula: C3H7N3O2 (117.0538242)

CAS ID: 352-97-6

L-Aspartate

Formula: C4H7NO4 (133.0375062)

CAS ID: 56-84-8

L-Glutamate 5-semialdehyde

Formula: C5H9NO3 (131.0582404)

CAS ID: 496-92-4

N-Acetyl-L-glutamate

Formula: C7H11NO5 (189.0637196)

CAS ID: 1188-37-0

N-Acetylornithine

Formula: C7H14N2O3 (174.1004374)

CAS ID: 6205-08-9

N-Carbamoylsarcosine

Formula: C4H8N2O3 (132.05348980000002)

CAS ID: 30565-25-4

N-Methylhydantoin

Formula: C4H6N2O2 (114.04292559999999)

CAS ID: 616-04-6

Phosphoguanidinoacetate

Formula: C3H8N3O5P (197.0201568)

CAS ID: 5115-19-5

Urea-1-carboxylate

Formula: C2H4N2O3 (104.0221914)

CAS ID: 625-78-5



Enzyme

EC Number name full name note
1.2.1.41 glutamate-5-semialdehyde dehydrogenase L-glutamate-5-semialdehyde:NADP+ 5-oxidoreductase (phosphorylating)
1.4.1.3 glutamate dehydrogenase [NAD(P)+] L-glutamate:NAD(P)+ oxidoreductase (deaminating)
1.5.1.2 pyrroline-5-carboxylate reductase L-proline:NAD(P)+ 5-oxidoreductase
1.5.8.3 sarcosine dehydrogenase sarcosine, 5,6,7,8-tetrahydrofolate:electron-transferflavoprotein oxidoreductase (demethylating,5,10-methylenetetrahydrofolate-forming)
2.1.1.2 guanidinoacetate N-methyltransferase S-adenosyl-L-methionine:N-guanidinoacetate methyltransferase
2.1.3.3 ornithine carbamoyltransferase carbamoyl-phosphate:L-ornithine carbamoyltransferase
2.1.4.1 glycine amidinotransferase L-arginine:glycine amidinotransferase
2.3.1.1 amino-acid N-acetyltransferase acetyl-CoA:L-glutamate N-acetyltransferase
2.5.1.16 spermidine synthase S-adenosyl 3-(methylthio)propylamine:putrescine 3-aminopropyltransferase
2.5.1.22 spermine synthase S-adenosyl 3-(methylthio)propylamine:spermidine 3-aminopropyltransferase
2.6.1.13 ornithine aminotransferase L-ornithine:2-oxo-acid aminotransferase
2.7.2.11 glutamate 5-kinase ATP:L-glutamate 5-phosphotransferase
2.7.3.2 creatine kinase ATP:creatine N-phosphotransferase
3.5.1.14 N-acyl-aliphatic-L-amino acid amidohydrolase N-acyl-aliphatic-L-amino acid amidohydrolase (carboxylate-forming)
3.5.3.1 arginase L-arginine amidinohydrolase
4.1.1.17 ornithine decarboxylase L-ornithine carboxy-lyase (putrescine-forming)
4.3.2.1 argininosuccinate lyase 2-(Nomega-L-arginino)succinate arginine-lyase (fumarate-forming)
6.3.4.16 carbamoyl-phosphate synthase (ammonia) carbon-dioxide:ammonia ligase (ADP-forming, carbamate-phosphorylating)
6.3.4.5 argininosuccinate synthase L-citrulline:L-aspartate ligase (AMP-forming)


Proteins

Protein ID name full name