Glycosaminoglycan metabolism

Clarke LA. The mucopolysaccharidoses: a success of molecular medicine. Expert Rev Mol Med. 2008 Jan 18;10():e1. doi: 10.1017/s1462399408000550. PMID: 18201392.; Cantz M, Gehler J. The mucopolysaccharidoses: inborn errors of glycosaminoglycan catabolism. Hum Genet. 1976 Jun 29;32(3):233–55. doi: 10.1007/bf00295816. PMID: 820626.

Metabolites

H+

Formula: H (1.0078246)

CAS ID: 12408-02-5

Sulfate

Formula: H2SO4 (97.9673812)

CAS ID: 7664-93-9

ATP(4-)

Formula: C10H12N5O13P3 (502.9644492)

CAS ID:

ADP(3-)

Formula: C10H12N5O10P2 (424.0059412)

CAS ID:



Enzyme

EC Number name full name note
2.7.1.25 adenylyl-sulfate kinase ATP:adenylyl-sulfate 3'-phosphotransferase


Proteins

Protein ID name full name
Q02196 MET14 Adenylyl-sulfate kinase