Glyoxylate metabolism and glycine degradation

Danpure CJ. Primary hyperoxaluria: from gene defects to designer drugs? Nephrol Dial Transplant. 2005 Aug;20(8):1525–9. doi: 10.1093/ndt/gfh923. PMID: 15956068.

Metabolites

CO2

Formula: CO2 (43.98983)

CAS ID: 124-38-9

H+

Formula: H (1.0078246)

CAS ID: 12408-02-5

H2O

Formula: H2O (18.0105642)

CAS ID: 7732-18-5

Hydrogen peroxide

Formula: H2O2 (34.0054792)

CAS ID: 7722-84-1

Oxygen

Formula: O2 (31.98983)

CAS ID: 7782-44-7

oxaloacetate(2-)

Formula: C4H2O5 (129.9902242)

CAS ID: 149-63-3

2-oxoglutarate(2-)

Formula: C5H4O5 (144.00587339999998)

CAS ID: 64-15-3

oxalate(2-)

Formula: C2O4 (87.97966)

CAS ID: 338-70-5

glycolate

Formula: C2H3O3 (75.00821880000001)

CAS ID: 666-14-8

pyruvate

Formula: C3H3O3 (87.00821880000001)

CAS ID: 57-60-3

glyoxylate

Formula: C2HO3 (72.9925696)

CAS ID:

NADPH(4-)

Formula: C21H26N7O17P3 (741.0598016)

CAS ID: 53-57-6

NAD(1-)

Formula: C21H26N7O14P2 (662.1012936000001)

CAS ID: 53-84-9

NADP(3-)

Formula: C21H25N7O17P3 (740.051977)

CAS ID: 53-59-8



Enzyme

EC Number name full name note
1.1.3.15 (S)-2-hydroxy-acid oxidase (S)-2-hydroxy-acid:oxygen 2-oxidoreductase
1.2.1.88 L-glutamate gamma-semialdehyde dehydrogenase L-glutamate gamma-semialdehyde:NAD+ oxidoreductase
1.2.3.5 glyoxylate oxidase glyoxylate:oxygen oxidoreductase
1.4.3.1 D-aspartate oxidase D-aspartate:oxygen oxidoreductase (deaminating)
1.4.3.3 D-amino-acid oxidase D-amino-acid:oxygen oxidoreductase (deaminating)
1.5.5.2 proline dehydrogenase L-proline:quinone oxidoreductase
1.5.5.3 hydroxyproline dehydrogenase trans-4-hydroxy-L-proline:quinone oxidoreductase
1.8.1.4 dihydrolipoyl dehydrogenase protein-N6-(dihydrolipoyl)lysine:NAD+ oxidoreductase
2.1.1.20 glycine N-methyltransferase S-adenosyl-L-methionine:glycine N-methyltransferase
2.3.1.61 dihydrolipoyllysine-residue succinyltransferase succinyl-CoA:enzyme-N6-(dihydrolipoyl)lysine S-succinyltransferase
2.6.1.1 aspartate transaminase L-aspartate:2-oxoglutarate aminotransferase
2.6.1.18 beta-alanine-pyruvate transaminase L-alanine:3-oxopropanoate aminotransferase
2.6.1.40 (R)-3-amino-2-methylpropionate-pyruvate transaminase (R)-3-amino-2-methylpropanoate:pyruvate aminotransferase
2.6.1.44 alanine-glyoxylate transaminase L-alanine:glyoxylate aminotransferase
2.6.1.51 serine-pyruvate transaminase L-serine:pyruvate aminotransferase
2.6.1.7 kynurenine-oxoglutarate transaminase L-kynurenine:2-oxoglutarate aminotransferase


Proteins

Protein ID name full name