EC: 1.1.99.39

D-2-hydroxyglutarate dehydrogenase ((R)-2-hydroxyglutarate:acceptor 2-oxidoreductase)

enzyme lambda metabolic reaction experiment

Pathways

pathway id name
BioCyc:ARA_PWYQT-1 lysine degradation III
PlantCyc:PLANT_PWYQT-1 lysine degradation III
PlantCyc:ARA_PWYQT-1 lysine degradation III
Reactome:R-BTA-1430728 Metabolism
Reactome:R-BTA-1428517 Aerobic respiration and respiratory electron transport
Reactome:R-MMU-1430728 Metabolism
Reactome:R-BTA-880009 Interconversion of 2-oxoglutarate and 2-hydroxyglutarate
Reactome:R-DRE-1430728 Metabolism
Reactome:R-DRE-1428517 Aerobic respiration and respiratory electron transport
Reactome:R-HSA-1428517 Aerobic respiration and respiratory electron transport
Reactome:R-MMU-1428517 Aerobic respiration and respiratory electron transport
Reactome:R-RNO-1430728 Metabolism
Reactome:R-RNO-1428517 Aerobic respiration and respiratory electron transport
Reactome:R-DRE-880009 Interconversion of 2-oxoglutarate and 2-hydroxyglutarate
Reactome:R-HSA-1430728 Metabolism
Reactome:R-HSA-880009 Interconversion of 2-oxoglutarate and 2-hydroxyglutarate
Reactome:R-MMU-880009 Interconversion of 2-oxoglutarate and 2-hydroxyglutarate
Reactome:R-RNO-880009 Interconversion of 2-oxoglutarate and 2-hydroxyglutarate
WikiPathways:WP4519 Cerebral organic acidurias, including diseases
PathBank:SMP0120726 Leigh Syndrome
PathBank:SMP0120842 Pyruvate Kinase Deficiency
PathBank:SMP0120753 Pyruvate Decarboxylase E1 Component Deficiency (PDHE1 Deficiency)
PathBank:SMP0120841 Primary Hyperoxaluria II, PH2
PathBank:SMP0087305 Pyruvaldehyde Degradation
PathBank:SMP0087325 Pyruvate Metabolism
PathBank:SMP0002359 The Oncogenic Action of D-2-Hydroxyglutarate in Hydroxyglutaric aciduria
PathBank:SMP0002434 Lysine Metabolism
PathBank:SMP0120751 Pyruvate Dehydrogenase Complex Deficiency