EC: 3.2.1.49

alpha-N-acetylgalactosaminidase (alpha-N-acetyl-D-galactosaminide N-acetylgalactosaminohydrolase)

enzyme lambda metabolic reaction experiment
uniprot:P17050 [alpha-N-acetylgalactosaminidase(Enzyme) wildtype]

Trihexosylceramide + H2O -> alpha_D_Galactose + beta_D_Galactosyl_1,4_beta_D_glucosylceramide
(( (Vmax * A) ) / (Km + A)) buffer: 0.1 M Sodium citrate, 9.3 mM Sodium taurocholate
PH: 4.3
Temperature: 37
uniprot:P17050 [alpha-N-acetylgalactosaminidase(Enzyme) wildtype]

N_Acetyl_D_galactosaminyl_N_Acetyl_D_galactosaminyl_1,3_D_galactosyl_1,4_D_galactosyl_1,4_D_glucosylceramide + H2O -> Globoside + N_Acetylgalactosamine
(( (Vmax * A) ) / (Km + A)) buffer: 0.1 M Sodium citrate, 7.4 mM Sodium taurocholate
PH: 3.9
Temperature: 37
uniprot:P17050 [alpha-N-acetylgalactosaminidase(Enzyme) wildtype]

Globopentaose + H2O -> N_Acetyl_D_galactosaminyl_1,3_D_galactosyl_1,4_D_galactosyl_1,4_D_glucopyranose + N_Acetylgalactosamine
(( (Vmax * A) ) / (Km + A)) buffer: Citrate/Phosphate
PH: 4.4
Temperature: 37
uniprot:P17050 [alpha-N-acetylgalactosaminidase(Enzyme) wildtype]

H2O + Globotriaose -> alpha_D_Galactose + beta_D_Galactosyl_1,4_beta_D_glucopyranose
(( (Vmax * A) ) / (Km + A)) buffer: Citrate/Phosphate
PH: 4.8
Temperature: 37

Pathways

pathway id name
PathBank:SMP0120702 Globoid Cell Leukodystrophy
PathBank:SMP0120738 Metachromatic Leukodystrophy (MLD)
PathBank:SMP0120810 Krabbe Disease
PathBank:SMP0087225 Galactose Metabolism
PathBank:SMP0120701 Gaucher Disease
PathBank:SMP0120809 Fabry Disease
PathBank:SMP0087337 Sphingolipid Metabolism
PathBank:SMP0087244 Sphingolipid Metabolism
PathBank:SMP0087320 Galactose Metabolism
PathBank:SMP0120699 Galactosemia