Carnitine Synthesis

Metabolites

2-Oxoglutarate

Formula: C5H6O5 (146.0215226)

CAS ID: 328-50-7

4-Trimethylammoniobutanal

Formula: C7H16NO (130.1231826)

CAS ID: 64595-66-0

4-Trimethylammoniobutanoate

Formula: C7H16NO2 (146.1180976)

CAS ID: 10329-41-6

CO2

Formula: CO2 (43.98983)

CAS ID: 124-38-9

H+

Formula: H (1.0078246)

CAS ID: 12408-02-5

H2O

Formula: H2O (18.0105642)

CAS ID: 7732-18-5

L-Carnitine

Formula: C7H15NO3 (161.105188)

CAS ID: 541-15-1

L-Lysine

Formula: C6H14N2O2 (146.1055224)

CAS ID: 56-87-1

NAD+

Formula: C21H28N7O14P2 (664.1169428000001)

CAS ID: 53-84-9

NADH

Formula: C21H29N7O14P2 (665.1247674)

CAS ID: 58-68-4

Oxygen

Formula: O2 (31.98983)

CAS ID: 7782-44-7



Enzyme

EC Number name full name note
1.14.11.8 trimethyllysine dioxygenase N6,N6,N6-trimethyl-L-lysine,2-oxoglutarate:oxygen oxidoreductase (3-hydroxylating)
1.2.1.24 succinate-semialdehyde dehydrogenase (NAD+) succinate-semialdehyde:NAD+ oxidoreductase
2.1.1.364 [histone H3]-lysine4 N-methyltransferase S-adenosyl-L-methionine:[histone H3]-L-lysine4 N6-methyltransferase
2.1.2.1 glycine hydroxymethyltransferase 5,10-methylenetetrahydrofolate:glycine hydroxymethyltransferase


Proteins

Protein ID name full name