Pyruvate Carboxylase Deficiency

Metabolites

2-Oxoglutarate

Formula: C5H6O5 (146.0215226)

CAS ID: 328-50-7

ADP

Formula: C10H15N5O10P2 (427.02941500000003)

CAS ID: 58-64-0

AMP

Formula: C10H14N5O7P (347.06308240000004)

CAS ID: 61-19-8

ATP

Formula: C10H16N5O13P3 (506.9957476)

CAS ID: 56-65-5

Glyoxylate

Formula: C2H2O3 (74.0003942)

CAS ID: 298-12-4

HCO3-

Formula: HCO3 (60.9925696)

CAS ID: 71-52-3

L-Alanine

Formula: C3H7NO2 (89.0476762)

CAS ID: 56-41-7

L-Glutamate

Formula: C5H9NO4 (147.0531554)

CAS ID: 56-86-0

Oxaloacetate

Formula: C4H4O5 (132.00587339999998)

CAS ID: 328-42-7

Pyruvate

Formula: C3H4O3 (88.0160434)

CAS ID: 127-17-3

diphosphate

Formula: O7P2 (173.911931)

CAS ID: 14000-31-8

phosphate(3-)

Formula: O4P (94.953423)

CAS ID: 14265-44-2



Enzyme

EC Number name full name note
6.-.-.-
6.1.1.7 alanine-tRNA ligase L-alanine:tRNAAla ligase (AMP-forming)


Proteins

Protein ID name full name