sphingolipid biosynthesis

Vallée B, Riezman H. Lip1p: a novel subunit of acyl-CoA ceramide synthase. EMBO J. 2005 Feb 23;24(4):730–41. PMID: 15692566; PMCID: PMC549621.; Kihara A, Igarashi Y. Identification and Characterization of aSaccharomyces cerevisiae Gene, RSB1, Involved in Sphingoid Long-chain Base Release. Journal of Biological Chemistry. 2002 Aug;277(33):30048–54. doi: 10.1074/jbc.m203385200.; Dickson RC, Lester RL. Sphingolipid functions in Saccharomyces cerevisiae. Biochimica et Biophysica Acta (BBA) - Molecular and Cell Biology of Lipids. 2002 Jun;1583(1):13–25. doi: 10.1016/s1388-1981(02)00210-x.; Kohlwein SD, Eder S, Oh C, Martin CE, Gable K, Bacikova D, Dunn T. Tsc13p Is Required for Fatty Acid Elongation and Localizes to a Novel Structure at the Nuclear-Vacuolar Interface in Saccharomyces cerevisiae. Molecular and Cellular Biology. 2001 Jan 01;21(1):109–25. doi: 10.1128/mcb.21.1.109-125.2001.

Metabolites

CO2

Formula: CO2 (43.98983)

CAS ID: 124-38-9

H+

Formula: H (1.0078246)

CAS ID: 12408-02-5

H2O

Formula: H2O (18.0105642)

CAS ID: 7732-18-5

Oxygen

Formula: O2 (31.98983)

CAS ID: 7782-44-7

palmitoyl-CoA(4-)

Formula: C37H62N7O17P3S (1001.3135592)

CAS ID: 1763-10-6

NADPH(4-)

Formula: C21H26N7O17P3 (741.0598016)

CAS ID: 53-57-6

NADP(3-)

Formula: C21H25N7O17P3 (740.051977)

CAS ID: 53-59-8



Enzyme

EC Number name full name note
1.-.-.-
1.1.1.102 3-dehydrosphinganine reductase D-erythro-dihydrosphingosine:NADP+ 3-oxidoreductase
1.14.18.6 4-hydroxysphinganine ceramide fatty acyl 2-hydroxylase (4R)-4-hydroxysphinganine ceramide,ferrocytochrome-b5:oxygen oxidoreductase (fatty acyl 2-hydroxylating)
1.14.18.7 dihydroceramide fatty acyl 2-hydroxylase dihydroceramide,ferrocytochrome-b5:oxygen oxidoreductase (fatty acyl 2-hydroxylating)
2.3.1.297 very-long-chain ceramide synthase very-long-chain fatty acyl-coA:sphingoid base N-acyltransferase
2.3.1.50 serine C-palmitoyltransferase palmitoyl-CoA:L-serine C-palmitoyltransferase (decarboxylating)
2.4.1.370 inositol phosphorylceramide mannosyltransferase GDP-alpha-D-mannose:(4R)-4-hydroxy-N-[(2R)-2-hydroxy-very-long-chain-acyl]-1-O-[(1D-myo-inositol-1-O-yl)hydroxyphosphoryl]sphinganine mannosyltransferase (configuration-retaining)
2.7.1.227 inositol phosphorylceramide synthase 1-phosphatidyl-1D-myo-inositol:a very-long-chain (2'R)-2'-hydroxy-phytoceramide phosphoinositoltransferase
2.7.1.228 mannosyl-inositol-phosphoceramide inositolphosphotransferase 1-phosphatidyl-1D-myo-inositol:(4R)-4-hydroxy-N-[(2R)-2-hydroxy-very-long-chain-acyl]-1-O-([6-O-(alpha-D-mannosyl)-1D-myo-inositol-1-O-yl]hydroxyphosphoryl)sphinganine phosphoinositoltransferase


Proteins

Protein ID name full name
P25045 LCB1 Serine palmitoyltransferase 1
P28496 LAC1 Ceramide synthase LAC1
P33300 SUR1 Mannosyl phosphorylinositol ceramide synthase SUR1
P36107 AUR1 Inositol phosphorylceramide synthase catalytic subunit AUR1
P38287 CSH1 Mannosyl phosphorylinositol ceramide synthase CSH1
P38342 TSC10 3-ketodihydrosphingosine reductase TSC10
P38703 LAG1 Ceramide synthase LAG1
P38954 IPT1 Inositolphosphotransferase 1
P38992 SUR2 Sphingolipid C4-hydroxylase SUR2
P40970 LCB2 Serine palmitoyltransferase 2
Q03529 SCS7 Ceramide very long chain fatty acid hydroxylase SCS7