Phenylalanine and tyrosine metabolism

Metabolites

Calcium cation

Formula: Ca (39.962591)

CAS ID: 14127-61-8

CO2

Formula: CO2 (43.98983)

CAS ID: 124-38-9

Fe2+

Formula: Fe (55.934939)

CAS ID: 15438-31-0

H+

Formula: H (1.0078246)

CAS ID: 12408-02-5

H2O

Formula: H2O (18.0105642)

CAS ID: 7732-18-5

Hydrogen peroxide

Formula: H2O2 (34.0054792)

CAS ID: 7722-84-1

Magnesium cation

Formula: Mg (23.98505)

CAS ID: 22537-22-0

Methanol

Formula: CH4O (32.0262134)

CAS ID: 67-56-1

Oxygen

Formula: O2 (31.98983)

CAS ID: 7782-44-7

2-oxo-3-phenylpropanoate

Formula: C9H7O3 (163.0395172)

CAS ID: 620-76-8

acetoacetate

Formula: C4H5O3 (101.02386800000001)

CAS ID: 141-81-1

2-oxoglutarate(2-)

Formula: C5H4O5 (144.00587339999998)

CAS ID: 64-15-3

butenedioate

Formula: C4H2O4 (113.99530920000001)

CAS ID: 17013-01-3

homogentisate

Formula: C8H7O4 (167.0344322)

CAS ID:

pyruvate

Formula: C3H3O3 (87.00821880000001)

CAS ID: 57-60-3

3-(4-hydroxyphenyl)pyruvate

Formula: C9H7O4 (179.0344322)

CAS ID: 622-54-8

NAD(1-)

Formula: C21H26N7O14P2 (662.1012936000001)

CAS ID: 53-84-9



Enzyme

EC Number name full name note
1.13.11.27 4-hydroxyphenylpyruvate dioxygenase 4-hydroxyphenylpyruvate:oxygen oxidoreductase (hydroxylating, decarboxylating)
1.13.11.5 homogentisate 1,2-dioxygenase homogentisate:oxygen 1,2-oxidoreductase (decyclizing)
1.14.16.1 phenylalanine 4-monooxygenase L-phenylalanine,tetrahydrobiopterin:oxygen oxidoreductase (4-hydroxylating)
1.4.3.2 L-amino-acid oxidase L-amino-acid:oxygen oxidoreductase (deaminating)
1.4.3.25 L-arginine oxidase L-arginine:oxygen oxidoreductase (deaminating)
1.5.1.34 6,7-dihydropteridine reductase 5,6,7,8-tetrahydropteridine:NAD(P)+ oxidoreductase
2.5.1.18 glutathione transferase RX:glutathione R-transferase
2.6.1.5 tyrosine transaminase L-tyrosine:2-oxoglutarate aminotransferase
2.6.1.64 glutamine-phenylpyruvate transaminase L-glutamine:phenylpyruvate aminotransferase
2.6.1.7 kynurenine-oxoglutarate transaminase L-kynurenine:2-oxoglutarate aminotransferase
3.4.19.5 beta-aspartyl-peptidase
3.5.1.1 asparaginase L-asparagine amidohydrolase
3.7.1.2 fumarylacetoacetase 4-fumarylacetoacetate fumarylhydrolase
4.2.1.96 4a-hydroxytetrahydrobiopterin dehydratase 4a-hydroxytetrahydrobiopterin hydro-lyase (6,7-dihydrobiopterin-forming)
4.4.1.13 cysteine-S-conjugate beta-lyase L-cysteine-S-conjugate thiol-lyase (deaminating; pyruvate-forming)
5.2.1.2 maleylacetoacetate isomerase 4-maleylacetoacetate cis-trans-isomerase


Proteins

Protein ID name full name